Exercise Physiology and Muscle Biology

1 Largest Two-Day CPET Study

  • Principal Investigator:: Multiple groups

  • Institution:: Multi-centre (USA)

  • Contact/URL:: https://doi.org/10.1186/s12967-024-05410-5

  • Funder:: Institutional

  • Status:: Published 2024

  • Phase:: Observational (physiological testing)

  • Cohort:: Largest 2-day CPET cohort in ME/CFS to date

  • Mechanism/Focus:: Two-day cardiopulmonary exercise testing to objectively measure post-exertional malaise. Significant reductions in VO2 and workload at the ventilatory anaerobic threshold (VAT) on day 2 in ME/CFS versus controls. Implicates autonomic dysregulation of blood flow and oxygen delivery for energy metabolism.

  • Primary Outcomes:: Impaired recovery after exertional stressor; cardiac, pulmonary, and metabolic contributions to exertion intolerance; larger effect sizes at VAT than peak

  • Estimated Completion:: Published

  • Publication Medium:: Journal of Translational Medicine

  • Document Relevance:: Ch. 6 (energy metabolism), Ch. 10 (cardiovascular), Ch. 20 (biomarker research—2-day CPET as objective PEM marker)

The 2-day CPET protocol remains the gold standard for objectively demonstrating PEM. This largest study to date substantiates that the day-2 decrement is reproducible across diverse ME/CFS cohorts (Keller et al. 2024). The finding that cardiac, pulmonary, and metabolic factors all contribute to exertion intolerance supports the multi-system model in Ch. 13 rather than any single-organ explanation.

2 Skeletal Muscle Properties in Long COVID and ME/CFS

  • Principal Investigator:: Multiple groups

  • Institution:: Multi-centre (Netherlands / Europe)

  • Contact/URL:: https://doi.org/10.1101/2025.05.02.25326885

  • Funder:: Institutional

  • Status:: Preprint May 2025

  • Phase:: Observational (muscle biopsy)

  • Cohort:: Long COVID and ME/CFS patients versus controls

  • Mechanism/Focus:: Muscle biopsies analysed for mitochondrial markers, WASF3 protein, ER stress markers. Found elevated WASF3 and ER stress with decreased mitochondrial Complex IV subunits. Critically, muscle abnormalities differed from those seen in bed rest deconditioning.

  • Primary Outcomes:: ME/CFS muscle pathology is distinct from deconditioning; WASF3 elevation confirmed in skeletal muscle tissue

  • Estimated Completion:: Preprint published; peer review pending

  • Publication Medium:: medRxiv

  • Document Relevance:: Ch. 6 (energy metabolism—WASF3), Ch. 17 (lifestyle interventions—exercise contraindications)

This study provides crucial evidence against the deconditioning hypothesis: if ME/CFS fatigue were due to simple disuse, muscle changes should resemble bed rest patterns (2025). The distinct pathology (WASF3 elevation, mitochondrial complex loss) aligns with the NIH WASF3 findings (Wang et al. 2023) and supports a disease-specific metabolic myopathy rather than secondary deconditioning.

References

2025. “Skeletal Muscle Properties in Long COVID and ME/CFS.” medRxiv. https://doi.org/10.1101/2025.05.02.25326885.
Keller, Betsy A, Candace N Receno, Carl J Franconi, Sebastian Harenberg, Jared Stevens, Xiangling Mao, Staci R Stevens, et al. 2024. “Cardiopulmonary and Metabolic Responses During a 2-Day CPET in Myalgic Encephalomyelitis/Chronic Fatigue Syndrome: Translating Reduced Oxygen Consumption to Impairment Status to Treatment Considerations.” Journal of Translational Medicine 22 (1): 627. https://doi.org/10.1186/s12967-024-05410-5.
Wang, Ping-yuan, Jin Ma, Young-Chae Kim, et al. 2023. WASF3 Disrupts Mitochondrial Respiration and May Mediate Exercise Intolerance in Myalgic Encephalomyelitis/Chronic Fatigue Syndrome.” Proceedings of the National Academy of Sciences 120 (34): e2302738120. https://doi.org/10.1073/pnas.2302738120.